Turkiye Klinikleri Journal of Pediatrics

.: ORIGINAL RESEARCH
Management of Uncommon Neck and Axillary Lipoblastomas in Children
Çocuklarda Nadir Boyun ve Koltuk Altı Lipoblastomlarının Yönetimi
Fatih AKOVAa, Emrah AYDINb, Murat BİNARc
aDepartment of Pediatric Surgery, Biruni University Faculty of Medicine, İstanbul, TURKEY
bDepartment of Pediatric Surgery, Koç University Faculty of Medicine, İstanbul, TURKEY
cClinic of Otorhinolaryngology, Medicana International İstanbul Hospital, İstanbul, TURKEY
Turkiye Klinikleri J Pediatr. 2021;30(2):99-104
doi: 10.5336/pediatr.2020-76782
Article Language: EN
Full Text
ABSTRACT
 Objective: Lipoblastomas are benign tumors developing from embryonic fat tissue with few cases reported in the head and neck region. Herein, we aim to present the management of a rare type of lipoblastoma in childhood. Material and Methods: A retrospective chart review was performed on all patients who were admitted due to a mass in the neck and axillary region between January 2015 and December 2019. Data were collected on demographics, comorbidities, preoperative characteristics, operative interventions, and postoperative complications and outcomes. The patients with lipoblastoma were further analyzed. Results: There were 52 patients operated on due to a mass in the neck or axillary region during the study time. The mean age was 5.42±4.16. The majority of the patients (40/52) were diagnosed with enlarged lymph nodes of which 32 (80%) were diagnosed with lymphoma. Among these populations, only two (3.8%) of them were diagnosed with lipoblastoma. Both cases were asymptomatic other than a painless mass. The histopathological examination confirmed the diagnosis of lipoblastoma after surgical excision. Both cases have been uneventful for four years postoperatively. Conclusion: In conclusion, lipoblastomas emerge as a slowly growing mass in early childhood and are mostly seen on the trunk and extremities. Although benign, they have the potential to increase in size and invade adjacent tissues. The gold standard treatment is complete surgical excision. Due to the possibility of recurrence, regular follow-up is strongly recommended after surgery.

Keywords: Lipoblastoma; childhood; head and neck; axillary; recurrence
ÖZET
 Amaç: Lipoblastom, embriyonik yağ hücrelerinden köken alan iyi huylu bir tümördür. Baş-boyun bölgesinde bildirilen vaka sayıları sınırlıdır. Bu çalışmada, nadir yerleşimli lipoblastoma yaklaşımı literatür ışığında sunmayı amaçladık. Gereç ve Yöntemler: Kliniğimize Ocak 2015 ve Aralık 2019 yılları arasında boyun ve koltuk altı bölgesinde şişlik ile başvuran hastaların dosyaları geriye dönük olarak incelendi. Olguların demografik özellikleri, eşlik eden hastalıkları, ameliyat bulguları, komplikasyonları ve son durumları belirlendi. Bu olgular arasında lipoblastom tanısı alanlar detaylı olarak analiz edildi. Bulgular: Belirtilen dönemde boyun ve koltuk altı bölgesinde şüpheli lezyon ile yaş ortalaması 5,42±4,16 yıl olan 52 hasta başvurdu. Hastaların büyük çoğunluğunda (40/52) büyümüş lenf nodu mevcuttu ve bu hastaların 32 (%80)'si lenfoma tanısı aldı. Bu hastalardan sadece 2 tanesi (%3,8) lipoblastom tanısı aldı. Her 2 olguda da başvuru anında ana şikâyet ağrısız büyüyen şişlik idi. Cerrahi eksizyon sonrası yapılan histopatolojik inceleme ile lipoblastom tanısı doğrulandı. Erken dönemde komplikasyon gözlenmeyen her 2 olgu da postoperatif 4. yılda sorunsuz takip edilmektedir. Sonuç: Lipoblastom, çocukluk çağında ağrısız büyüyen, çoğunlukla gövde ve ekstremiteleri tutan bir lezyondur. İyi huylu olmasına rağmen büyüme ve çevre dokulara invaze olma eğilimindedir. Cerrahi olarak çıkarılması tedavide altın standarttır. Nüks etme ihtimali nedeni ile uzun süreli takip önerilmektedir.

Anahtar Kelimeler: Lipoblastom; çocuk; baş boyun; koltuk altı; nüks
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