Cystic fibrosis is a genetic disease in children. The respiratory system is affected due to thickening of secretions. Therefore, pulmonary functions are deteriorated and dyspnea may occur during exercise. Children with cystic fibrosis may not tolerate exercise. Exercise testing is important to determine exercise-related complications and to plan exercise. Exercise tests are necessary applications for all individuals engaged in exercise. Exercise tests are used to determine the prognosis of the disease, exercise tolerance, mortality, efficacy of the treatment and exercise prescription. In this review, the studies using exercise test with children with cystic fibrosis aged between 4 and 18 years were examined. The subjects related to exercise and exercise test are briefly mentioned. The studies have been published between 1986 and 2018 years. The purpose of this review is to emphasize the importance of exercise tests in children with cystic fibrosis and to examine the various exercise tests used in previous studies. In this study, laboratory and field tests were used. Laboratory tests were performed using bicycle ergometers and treadmill. Wingate, Godfrey, CPETSRT and Bruce protocol were used in laboratory tests. In the field tests, generally 6 minutes walk test, 2 minutes walk test, 3 minutes step test, Munich fitness test and shuttle test were used. These protocols were selected according to the age, height and weight of the child. These tests were modified for children.
Keywords: Children; cystic fibrosis; exercise test
Kistik fibrozis çocuklarda görülen genetik bir hastalıktır. Sekresyonların kalınlaşmasından dolayı solunum sistemi etkilenir. Bu nedenle, pulmoner fonksiyonlar bozulur ve egzersiz sırasında dispne meydana gelebilir. Kistik fibrozisli çocuklar egzersizi tolere edemeyebilir. Egzersize bağlı komplikasyonları belirlemek ve egzersiz planlaması yapabilmek için egzersiz testi önemlidir. Egzersiz testleri egzersiz yapan tüm bireyler için gerekli bir uygulamadır. Egzersiz testleri hastalığın prognozunu, egzersiz toleransını, mortaliteyi, tedavinin etkinliğini ve egzersiz reçetesini belirlemede kullanılır. Bu derleme çalışmasında, 4-18 yaş arası kistik fibrozisli çocuklarla yapılan egzersiz testi kullanılan çalışmalar incelenmiştir. Egzersiz ve egzersiz testi ile ilgili konulara kısaca değinilmiştir. İncelenen çalışmalar 1986 ile 2018 yılları arasında yayınlanmıştır. Derlemenin amacı kistik fibrozisli çocuklarda egzersiz testinin önemini vurgulamak ve daha önceki çalışmalarda kullanılan çeşitli egzersiz testlerini incelemektir. Bu çalışmada laboratuvar ve alan testleri kullanılmıştır. Laboratuvar testleri bisiklet ergometresi ve koşu bandı kullanılarak uygulanmıştır. Laboratuvar testlerinde Wingate, Godfrey, CPET-SRT ve Bruce protokolü kullanılmıştır. Alan testlerinde ise genellikle 6 dakika yürüme testi, 2 dakika yürüme testi, 3 dakika step testi, Münih fitnes testi ve mekik testi kullanılmıştır. Bu protokoller çocuğun yaşına, boyuna ve kilosuna göre seçilmiştir. Testler çocuklar için modifiye edilmiştir.
Anahtar Kelimeler: Çocuk; kistik fibrozis; egzersiz testi
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