Objective: Bicuspid aortic valve (BAV), which is the one of the most common congenital heart malformation and seen approximately 1-2% of the general population. It has been shown that BAV is associated aortic valve dysfunction (aortic stenosis, aortic regurgitation or both) and increased risk for bacterial endocarditis from adult to the advanced ages. In this study, we aimed to determine the frequency of BAV disease in the asymptomatic young population who is applied to the health board. Material and Methods: 5,490 subjects who were consulted to the cardiology outpatient by health board were systematically analyzed from our hospital database system and 15 patients with BAV were identified. The frequency of BAV and aortic valve measurments were recorded. Patients with previous aortic valve intervention were excluded from the study. Results: Fifteen patients with BAV were identified (0.3%), all patients were newly diagnosed during screening at the health board. Mean age of the BAV subjects was 23.4±2.45 years. Two of them were female (13.3%) and thirteen of them (86.7%) were male. Aortic insufficiency was the most common pathology, mild in 11 (73.3%), and moderate in 2 (13.3%) cases. Only 2 (13.3%) patients had aortic dilatation. Aortic stenosis was not detected. Conclusion: Prevalence of BAV in asymptomatic young adults was lower than the literature.
Keywords: Bicuspid aortic valve disease; aortic valve stenosis; aortic valve insufficiency
Amaç: Biküspit aort kapak (BAK) en sık görülen konjenital kalp hastalıklarından biridir ve genel popülasyonda %1-2 oranında görülür. BAK'ın yetişkinlikten ilerleyen yaşlara doğru aort kapak disfonksiyonu (aort stenozu, aort yetersizliği veya her ikisi) ve artmış infektif endokardit riski ile birlikte olduğu gösterilmiştir. Bu çalışmada, sağlık kuruluna başvuran asemptomatik genç erişkinlerde BAK sıklığını araştırmayı amaçladık. Gereç ve Yöntemler: Kardiyoloji polikliniğine sağlık kurulu muayenesi amacı ile başvuran 5.490 hastanın verisi tarandı ve 15 BAK hastası tespit edildi. BAK sıklığı ve aort kapak ölçümleri kaydedildi. Daha önceden aort kapak müdahalesi geçiren hastalar çalışmadan dışlandı. Bulgular: Sağlık kuruluna başvuran hastaların 15'inde BAK (%0,3) saptandı. Bu hastaların hepsi yeni teşhis edilen hastalardı. Hastaların ortalama yaşı 23,4±2,45 yıl idi. Hastaların 2'si (%13,3) kadın, 13'ü (%86,7) erkekti. En sık patoloji aort yetersizliği idi ve 11 (%73,3) hastada hafif, 2 (%13,3) hastada orta derecede saptandı. İki (%13,3) hastada aort genişlemesi saptandı. Aort darlığı hiçbir hastada saptanmadı. Sonuç: BAK prevalansı asemptomatik genç kişilerde literatürde belirtilen orandan daha düşük bulunmuştur.
Anahtar Kelimeler: Biküspit aort kapak hastalığı; aort kapak stenozu; aort kapağı yetersizliği
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