Turkiye Klinikleri Journal of Ophthalmology

.: CASE REPORTS
Matür Katarakt Ameliyatı Sonrası İnsidental Tespit Edilen Straatsma Olgusu
An Incidentally Detected Straatsma Syndrome Case After Mature Cataract Surgery
Ali ŞİMŞEKa, Çağrı MUTAFa, Eren HÜZMELİa, Ekrem Can ARABACIa
aHarran Üniversitesi Tıp Fakültesi, Göz Hastalıkları ABD, Şanlıurfa, Türkiye
Turkiye Klinikleri J Ophthalmol. 2022;31(3):191-5
doi: 10.5336/ophthal.2021-87114
Article Language: TR
Full Text
ÖZET
Bu olgu sunumunda, çocukluğundan beri sağ gözünde görme azlığı olan ve Straatsma sendromu tanısı alan 23 yaşında bir kadın hastanın bulgularından bahsedilmiştir. Hasta, sağ gözünde görme kaybı ve beyazlık oluşması şikâyetleriyle kliniğimize başvurdu. Görme keskinliği sağ gözde ışık hissi düzeyinde, sol gözde ise 10/10 seviyesindeydi. Direkt ve indirekt ışık refleksleri pozitifti. Biyomikroskobik muayenesinde sağ gözde matür kataraktı vardı. Sol göz doğal bulundu. Göz içi basınçları sağ gözde 16 mmHg, sol gözde 18 mmHg idi. Fundus muayenesinde sağ göz dibi matür katarakt nedeniyle aydınlanmıyordu. Sol göz dibi doğal bulundu. Sağ göze yapılan orbital ultrasonografi doğal olarak bulundu. Retina yatışıktı. Bununla birlikte sağ gözde 35 prizm diyoptri ekzotropya mevcuttu. Göz hareketleri her yöne serbestti. Hastaya görme keskinliğini artırmak amacıyla fakoemülsifikasyon ameliyatı yapıldı ve postoperatif dönemde beklenen vizyon artışının olmadığı görüldü. Hastalık, çocukluk çağında fark edilmemiş olmasına rağmen ambliyopinin düzeltilebilmesi için hasta göz kapama uygulaması ve nörovizyon tedavilerinden fayda görebilir.

Anahtar Kelimeler: Katarakt; miyopi; strabismus; miyelinli sinir lifleri; ambliyopi
ABSTRACT
In this case report, the findings of a 23-year-old female patient who had vision loss in her right eye since childhood and was diagnosed with Straatsma syndrome were mentioned. The patient applied to our clinic with complaints of vision loss and whiteness in the right eye. Visual acuity was at the level of light sensation in the right eye and 10/10 in the left eye. Direct and indirect light reflexes were positive. In the biomicroscopy examination, there was a mature cataract in the right eye. The left eye was found to be normal. Intraocular pressures were 16 mmHg in the right eye and 18 mmHg in the left eye. Fundus of the right eye was not illuminated due to mature cataract. Fundus of the left eye was found to be normal. Orbital ultrasonography of the right eye was found normal. Retina was intact. However, there was exotropia at the level of 35 prizm dioptri in the right eye. Eye movements were free in all directions. The patient underwent phacoemulsification surgery to improve visual acuity and it was observed that there was no expected increase in visual acuity in the postoperative period. Although the disease cannot be noticed in childhood, it may benefit from eye closure application and neurovision treatments to correct amblyopia.

Keywords: Cataract; myopia; strabismus; myelinated nerve fibers; amblyopia
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